Search results
Results from the WOW.Com Content Network
Corneal dystrophy-perceptive deafness syndrome, also known as Harboyan syndrome, is a rare genetic disorder characterized by congenital hereditary corneal dystrophy that occurs alongside progressive hearing loss of post-lingual onset.
The social model of deafness stems from the social model of disability. The concept of social disability was created by people who are disabled themselves, their families, friends, and associated social and political networks. Professionals in the human services fields and the social sciences greatly contributed to the social model. This model ...
Cerebral deafness (also known as cortical deafness or central deafness) is a disorder characterized by complete deafness that is the result of damage to the central nervous system. The primary distinction between auditory agnosia and cerebral deafness is the ability to detect pure tones, as measured with pure tone audiometry.
A family of metrics for speech intelligibility, [263] speech quality, [267] [268] and music quality [269] has been derived using a shared model of the auditory periphery [270] that can represent hearing loss. Using a model of the impaired periphery leads to more accurate predictions for hearing-impaired listeners than using a normal-hearing ...
Change deafness is a perceptual phenomenon that occurs when, under certain circumstances, a physical change in an auditory stimulus goes unnoticed by the listener. There is uncertainty regarding the mechanisms by which changes to auditory stimuli go undetected, though scientific research has been done to determine the levels of processing at which these consciously undetected auditory changes ...
Sensorineural hearing loss (SNHL) is a type of hearing loss in which the root cause lies in the inner ear, sensory organ (cochlea and associated structures), or the vestibulocochlear nerve (cranial nerve VIII). SNHL accounts for about 90% of reported hearing loss.
The shape of the audiogram resulting from pure-tone audiometry gives an indication of the type of hearing loss as well as possible causes. Conductive hearing loss due to disorders of the middle ear shows as a flat increase in thresholds across the frequency range. Sensorineural hearing loss will have a contoured shape depending on the cause.
This condition was first discovered in 1995 by Melberg et al. when they described 5 members of a 4-generation Swedish family where cerebellar ataxia and sensorineural deafness presented as an autosomal dominant trait, 4 of them had narcolepsy and 2 had diabetes mellitus. The oldest members had psychiatric symptoms, neurological anomalies, and ...