enow.com Web Search

  1. Ad

    related to: alpha ketoglutarate deficiency symptoms

Search results

  1. Results from the WOW.Com Content Network
  2. Hyperlysinemia - Wikipedia

    en.wikipedia.org/wiki/Hyperlysinemia

    Hyperlysinemia has an autosomal recessive pattern of inheritance. Hyperlysinemia is inherited in an autosomal recessive manner. [2] This means the defective gene responsible for the disorder is located on an autosome, and two copies of the defective gene (one inherited from each parent) are required in order to be born with the disorder.

  3. α-Ketoglutaric acid - Wikipedia

    en.wikipedia.org/wiki/Α-Ketoglutaric_acid

    α-Ketoglutarate is a component of the citric acid cycle, a cyclical metabolic pathway located in the mitochondria.This cycle supplies the energy that cells need by sequentially metabolizing (indicated by →) citrate through seven intermediate metabolites and then converting the eighth intermediate metabolite, oxaloacetate, back to citrate: [2]

  4. OGDH - Wikipedia

    en.wikipedia.org/wiki/OGDH

    Alpha-ketoglutarate dehydrogenase also known as 2-oxoglutarate dehydrogenase E1 component, mitochondrial is an enzyme that in humans is encoded by the OGDH gene. [ 5 ] [ 6 ] [ 7 ] Structure

  5. Branched-chain alpha-keto acid dehydrogenase complex

    en.wikipedia.org/wiki/Branched-chain_alpha-keto...

    This enzyme complex catalyzes the oxidative decarboxylation of branched, short-chain alpha-ketoacids. BCKDC is a member of the mitochondrial α-ketoacid dehydrogenase complex family, which also includes pyruvate dehydrogenase and alpha-ketoglutarate dehydrogenase, key enzymes that function in the Krebs cycle.

  6. Isocitrate dehydrogenase - Wikipedia

    en.wikipedia.org/wiki/Isocitrate_dehydrogenase

    Isocitrate dehydrogenase (IDH) (EC 1.1.1.42) and (EC 1.1.1.41) is an enzyme that catalyzes the oxidative decarboxylation of isocitrate, producing alpha-ketoglutarate (α-ketoglutarate) and CO 2. This is a two-step process, which involves oxidation of isocitrate (a secondary alcohol ) to oxalosuccinate (a ketone ), followed by the ...

  7. Wernicke–Korsakoff syndrome - Wikipedia

    en.wikipedia.org/wiki/Wernicke–Korsakoff_syndrome

    Thiamine deficiency is also related to malnutrition from poor diet, impaired use of thiamine by the cells and impaired storage in the liver. [25] Without thiamine the Krebs cycle enzymes pyruvate dehydrogenase complex (PDH) and alpha-ketoglutarate dehydrogenase (alpha-KGDH) are impaired. [15]

  8. Vitamin B12 deficiency symptoms - AOL

    www.aol.com/finance/vitamin-deficiency-cause...

    Vitamin B12 deficiency symptoms . Vitamin B12 deficiency has a few hallmark symptoms, according to doctors: Lack of energy. Mental fatigue. Nausea, vomiting, or diarrhea. Lack of appetite. Weight loss

  9. Oxoglutarate dehydrogenase complex - Wikipedia

    en.wikipedia.org/wiki/Oxoglutarate_dehydrogenase...

    α-ketoglutarate + NAD + + CoA → Succinyl CoA + CO 2 + NADH Oxoglutarate dehydrogenase (α-Ketoglutarate dehydrogenase) This reaction proceeds in three steps: decarboxylation of α-ketoglutarate, reduction of NAD + to NADH, and subsequent transfer to CoA, which forms the end product, succinyl CoA. ΔG°' for this reaction is -7.2 kcal mol −1.

  1. Ad

    related to: alpha ketoglutarate deficiency symptoms