Search results
Results from the WOW.Com Content Network
Ileal atresia – malformation of the ileum, the lower part of the small intestine; Colon atresia – malformation of the colon; Malformations may also occur along multiple portions of the intestinal tract; for instance a malformation that occurs along or spans the length of the jejunum and the ileum is termed jejunoileal atresia. [5] [3]
Strømme syndrome is a very rare autosomal recessive genetic condition characterised by intestinal atresia (in which part of the intestine is missing), eye abnormalities and microcephaly. The intestinal atresia is of the "apple-peel" type, in which the remaining intestine is twisted around its main artery.
The majority of cases are small intestinal atresia, while colonic atresias are uncommon. [14] There have been two main etiologies proposed for intestinal atresia: the first is a lack of re-vacuolization of the solid cord stage of intestinal development, and the second is a late intrauterine mesenteric vascular accident.
In adults, Crohn's disease is a ... and to prevent SBS upon the initial repair of certain types of intestinal atresia. ... and five had received intestinal ...
Short bowel syndrome in adults and children is most commonly caused by surgery (intestinal resection). [4] In those who undergo intestinal resection, approximately 15% eventually develop small bowel syndrome (75% of those due to 1 large resection and 25% due to multiple separate intestinal resections). [4] This surgery may be done for:
The procedure involves counterclockwise detorsion of the bowel, surgical division of Ladd's bands (shown in image), widening of the small intestine's mesentery, performing an appendectomy, and reorientation of the small bowel on the right and the cecum and colon on the left (the appendectomy is performed so as not to be confused by atypical ...
Familial multiple intestinal atresia (FMIA) or familial intestinal polyatresia syndrome (FIPA) is an inherited disorder where atresia occurs at multiple locations throughout the small and large intestines. It presents at birth and the prognosis is very poor with almost all those diagnosed with this condition dying with one month.
There is no standard treatment for TTC7A Deficiency at this time. Management of TTC7A deficiency currently entails bowel resection for any atresias, hematopoietic stem cell transplantation to correct the immunodeficiencies and immunosuppression to help alleviate bowel disease and immune disregulation.