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Gerstmann–Sträussler–Scheinker syndrome (GSS) is an extremely rare, always fatal (due to it being caused by prions) neurodegenerative disease that affects patients from 20 to 60 years in age. It is exclusively heritable, and is found in only a few families all over the world. [ 1 ]
TSEs of humans include Creutzfeldt–Jakob disease, Gerstmann–Sträussler–Scheinker syndrome, fatal familial insomnia, and kuru, as well as the recently discovered variably protease-sensitive prionopathy and familial spongiform encephalopathy. Creutzfeldt-Jakob disease itself has four main forms, the sporadic (sCJD), the hereditary/familial ...
Gerstmann syndrome is a neurological disorder that is characterized by a constellation of symptoms [1] that suggests the presence of a lesion usually near the junction of the temporal and parietal lobes at or near the angular gyrus. Gerstmann syndrome is typically associated with damage to the inferior parietal lobule of the dominant hemisphere ...
Lesions to the left angular gyrus are associated with finger agnosia, as well as the other symptoms of Gerstmann Syndrome, also known as Angular Gyrus Syndrome. In a study by Rusconi et al., repetitive transcranial magnetic stimulation was used in healthy individuals to simulate finger agnosia. Stimulation to the intraparietal sulcus ...
Gerstmann–Sträussler–Scheinker syndrome – usually a change in codon 102 from proline to leucine [52] fatal familial insomnia – aspartic acid-178 is replaced by asparagine while methionine is present at amino acid 129 [53]
Here are links to possibly useful sources of information about Gerstmann–Sträussler–Scheinker syndrome. PubMed provides review articles from the past five years (limit to free review articles) The TRIP database provides clinical publications about evidence-based medicine. Other potential sources include: Centre for Reviews and ...
Gastrointestinal syndrome; Genitopatellar syndrome; Gerstmann syndrome; Gerstmann–Sträussler–Scheinker syndrome; Geschwind syndrome; Gianotti–Crosti syndrome; Giant platelet disorder; Guillain–Barré syndrome; Gillespie syndrome; Gitelman syndrome; Gleich's syndrome; GMS syndrome; Goldberg–Shprintzen syndrome; Goldenhar syndrome
In 1936 with neurologists Josef Gerstmann (1887–1969) and Ilya Scheinker (1902–1954), he described a rare prion disease that is usually regarded as a variant of Creutzfeldt–Jakob disease. Today this condition is known as Gerstmann–Sträussler–Scheinker syndrome (GSS). [3]